Primitive Myxoid Mesenchymal Tumor of Infancy
نویسندگان
چکیده
منابع مشابه
A cooperative approach to diagnosis of rare diseases: primitive myxoid mesenchymal tumor of infancy.
Primitive Myxoid Mesenchymal Tumor of Infancy (PMMTI) is a recently recognized locally aggressive myofibroblastic tumor. It is a low- to intermediate-grade fibroblastic malignancy with a high local recurrence rate but low metastatic potential and is composed of primitive spindled cells in a myxoid background. We present the eleventh reported case of PMMTI, occurring in the sinonasal tract of a ...
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A girl, aged 19 months, presented with a sacrococcygeal tumor that developed at 5 months after birth and gradually enlarged. Serum tumor marker levels were negative. Ultrasound imaging showed abundant blood flow in the tumor. However, neither computed tomography (CT) nor magnetic resonance imaging (MRI) showed contrast agent incorporation. The surgically resected tumor consisted of immature cel...
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Primitive myxoid mesenchymal tumor of the infancy (PMMTI) is an extremely rare soft tissue tumor. We report a case of 2-year-old girl presenting with omentum and intestinal wall involvement in abdominal cavity with prominent refractory ascites. Histologically, the tumor consisted of primitive spindle or polygonal cells dispersing in a myxoid background with delicate blood vessels. Immunohistoch...
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The primitive neuroectodermal tumor (PNET) belongs to a group of highly malignant tumors and is composed of small round cells of a neuroectodermal origin. Categorized in the same tumor family as Ewing sarcoma, the PNET is most likely to occur in bones and soft tissues. However, a small number of PNET cases arising in the pelvis have been reported as well. We present three cases of pelvic PNET: ...
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ژورنال
عنوان ژورنال: Journal of Pediatric Surgery Case Reports
سال: 2020
ISSN: 2213-5766
DOI: 10.1016/j.epsc.2020.101643